Abstract

The diagnosis and management of idiopathic pulmonary fibrosis

Idiopathic pulmonary fibrosis (IPF) is one of the most often diagnosed interstitial lung diseases. IPF tends to affect people aged over 60 years with a history of smoking. The progressive nature of IPF leads to diminished quality of life and shorter life expectancy. Advancements in the diagnostic criteria and a greater access to high-resolution computed tomography allow an earlier and more confident diagnosis. In addition, antifibrotic treatment holds the promise of increasing the duration and quality of life. This paper discusses the present diagnostic criteria and possible treatment options.

Piśmiennictwo

1. Piotrowski WW, Bestry I, Białas AJ i wsp. Wytyczne Polskiego Towarzystwa Chorób Płuc dotyczące diagnostyki i leczenia idiopatycznego włóknienia płuc. Pneumonologia Polska 2020;1:9-67

2. Raghu G, Remy-Jardin M, Myers JL, et al. Diagnosis of Idiopathic Pulmonary Fibrosis. An Official ATS/ERS/JRS/ALAT Clinical Practice Guideline. Am J Respir Crit Care Med 2018;198:e44-e68. doi: 10.1164/rccm.201807-1255ST

3. Lynch DA, Sverzellati N, Travis WD, et al. Diagnostic Criteria for Idiopathic Pulmonary Fibrosis: A Fleischner Society White Paper. The Lancet Respiratory Medicine 2018;6:138-53. doi: 10.1016/S2213-2600(17)30433-2

4. Raghu G, Collard HR, Egan JJ, et al. An Official ATS/ERS/JRS/ALAT Statement: Idiopathic Pulmonary Fibrosis: Evidence-Based Guidelines for Diagnosis and Management. Am J Respir Crit Care Med 2011;183:788-824. doi: 10.1164/rccm.2009-040GL

5. Wood DE, Kazerooni EA, Baum SL, et al. Lung Cancer Screening, Version 3.2018, NCCN Clinical Practice Guidelines in Oncology. Journal of the National Comprehensive Cancer Network 2018;16:412-41. doi: 10.6004/jnccn.2018.0020

6. Rzyman W, Didkowska J, Dziedzic R, et al. Wytyczne i zalecenia zespołu ekspertów dotyczące wykrywania wczesnego raka płuca w Polsce. Advances in Respiratory Medicine 2018;86:50-72

7. Raghu G, Rochwerg B, Zhang Y, et al. An Official ATS/ERS/JRS/ALAT Clinical Practice Guideline: Treatment of Idiopathic Pulmonary Fibrosis. An Update of the 2011 Clinical Practice Guideline. Am J Respir Crit Care Med 2015;192:e3-e19. doi: 10.1164/rccm.201506-1063ST

8. Laporta Hernandez R, Aguilar Perez M, Lázaro Carrasco MT, et al. Lung Transplantation in Idiopathic Pulmonary Fibrosis. Med Sci (Basel) 2018;6. doi: 10.3390/medsci6030068

9. Wong AW, Fidler L, Marcoux V, et al. Practical Considerations for the Diagnosis and Treatment of Fibrotic Interstitial Lung Disease During the Coronavirus Disease 2019 Pandemic. Chest 2020;158:1069-78. doi: 10.1016/j.chest.2020.04.019

10. Spencer L. Advice for Managing Interstitial Lung Disease Patients during COVID-19 Pandemic. https://www.brit-thoracic.org.uk/media/455101/bts-management-advice-for-ild-patients-v10-23-march-2020.pdf

Do góry